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ID 31823
JaLCDOI
フルテキストURL
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著者
Tanaka, Masato Department of Orthopaedic Surgery, Okayama University Hospital
Nakanishi, Kazuo Department of Orthopaedic Surgery, Okayama University Hospital
Sugimoto, Yoshihisa Department of Orthopaedic Surgery, Okayama University Hospital
Misawa, Haruo Department of Orthopaedic Surgery, Okayama University Hospital
Takigawa, Tomoyuki Department of Orthopaedic Surgery, Okayama University Hospital
Nishida, Keiichiro Department of Human Morphology, Okayama University Graduate School of Medicine, Dentistry and Pharmaceutical Sciences Kaken ID publons researchmap
Ozaki, Toshifumi Department of Orthopaedic Surgery, Okayama University Hospital Kaken ID publons researchmap
抄録

Scoliosis is a common clinical manifestation of Rett syndrome, a neurodevelopmental disorder that almost exclusively affects females. The spinal curve in patients with Rett syndrome is typically a long C curve of a neuromuscular type. As the onset of the scoliosis is very early and shows rapid progression, early surgical intervention has been recommended to prevent a life-threatening collapsing spine syndrome. However, there are high perioperative risks in Rett syndrome patients who undergo spinal surgery, such as neurological compromise and respiratory dysfunction due to rigid spinal curve. We herein report the surgical result of treating severe rapid progressive thoracic scoliosis in a 16-year-old girl with Rett syndrome. Posterior segmental pedicle screw fixation was performed from T1 to L3 using a computer-assisted technique. Post-operative radiography demonstrated a good correction of the curve in both the sagittal and coronal alignment. There were no postoperative complications such as neurological compromise. The patient had maintained satisfactory spinal balance as of the 3-year follow-up examination.

キーワード
Rett syndrome
scoliosis
computer navigation-assisted surgery
segmental pedicle screw fixation
Amo Type
Case Report
発行日
2009-12
出版物タイトル
Acta Medica Okayama
63巻
6号
出版者
Okayama University Medical School
開始ページ
373
終了ページ
377
ISSN
0386-300X
NCID
AA00508441
資料タイプ
学術雑誌論文
言語
English
論文のバージョン
publisher
査読
有り
PubMed ID
Web of Science KeyUT