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ID 31823
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Author
Nakanishi, Kazuo
Sugimoto, Yoshihisa
Misawa, Haruo
Takigawa, Tomoyuki
Nishida, Keiichiro Kaken ID researchmap
Ozaki, Toshifumi Kaken ID researchmap
Abstract

Scoliosis is a common clinical manifestation of Rett syndrome, a neurodevelopmental disorder that almost exclusively affects females. The spinal curve in patients with Rett syndrome is typically a long C curve of a neuromuscular type. As the onset of the scoliosis is very early and shows rapid progression, early surgical intervention has been recommended to prevent a life-threatening collapsing spine syndrome. However, there are high perioperative risks in Rett syndrome patients who undergo spinal surgery, such as neurological compromise and respiratory dysfunction due to rigid spinal curve. We herein report the surgical result of treating severe rapid progressive thoracic scoliosis in a 16-year-old girl with Rett syndrome. Posterior segmental pedicle screw fixation was performed from T1 to L3 using a computer-assisted technique. Post-operative radiography demonstrated a good correction of the curve in both the sagittal and coronal alignment. There were no postoperative complications such as neurological compromise. The patient had maintained satisfactory spinal balance as of the 3-year follow-up examination.

Keywords
Rett syndrome
scoliosis
computer navigation-assisted surgery
segmental pedicle screw fixation
Amo Type
Case Report
Published Date
2009-12
Publication Title
Acta Medica Okayama
Volume
volume63
Issue
issue6
Publisher
Okayama University Medical School
Start Page
373
End Page
377
ISSN
0386-300X
NCID
AA00508441
Content Type
Journal Article
language
英語
File Version
publisher
Refereed
True
PubMed ID
Web of Science KeyUT